Japanese Biliary Atresia Registry, 1989 to 1994
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MOHAMED IBRAHIM, TAKESHI
MIYANO, RYOJI OHI;
MORIHIRO SAEKI, KAZUO
SHIRAKI, KOICHI TANAKA,
TAKAMICHI KAMIYAMA and
MASAKI NIO
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The Japanese Biliary Atresia Society, Sendai 980 - 77
The Japanese Biliary Atresia Society founded in 1980 for the aim of investigations of all
aspects of biliary atresia (BA), started a nationwide registry of BA patients in 1989. A total
of 626 cases were registered from 1989 to 1994. The male to female ratio was 0.58.
Corrective surgery was performed in 603 patients. Regarding the type of obstruction, 63
cases were Type I, atresia of the common bile duct, 9 were Type II, atresia of the hepatic
ducts, and 543 were Type III, atresia of the porta hepatis. As initial corrective procedures,
original Roux-en Y, Suruga II and Roux-en Y with intestinal valve were mainly employed.
Jaundice cleared in 346 patients (57%) and decreased in 131, while it persisted in 120. The
5-year-follow-up showed that 34 patients, 49% of the patients who were followed up, were
alive without jaundice, while 28 (41% ) are dead. Thirty five, 33% of the patients who were
entered to the Registry, were lost to follow-up.
Key word(s)---
biliary atresia; registry; Japan
Tohoku J. Exp. Med., 1997, 181, 85-95
Address for reprints:
Ryoji Ohi, M.D., Department of Pediatric Surgery, Tohoku University School of medicine,
1-1 Seiryomachi, Aoba-ku, Sendai 980-77, Japan.
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